Persistent fetal vasculature (PFV) is a group of abnormal clinical manifestations associated with the failure of the regression of fetal vasculature. Clinical manifestations can include such conditions as persistent pupillary membranes, persistent posterior fetal fibrovascular sheath of the lens, Mittendorf dot,
Bergmeister papilla, macular abnormalities, optic nerve abnormalities, retinal folds and so on, most of which are accompanied by lens opacity. PFV can present in three forms: purely anterior, purely posterior or a combination of both. Due to the scarcity of clinical cases and the heterogeneity of clinical manifestations, an accurate diagnosis and appropriate treatment have a marked effect on a patient's prognosis. With the fertility boom after the second child policy, there may be an increase in the number of children with PFV. The purpose of this review is to discuss the clinical manifestations, diagnosis, types and treatment, to standardize the diagnosis and treatment, and to improve the curative prognosis of PFV.
赵云娥,胡曼. 重视婴幼儿永存胚胎血管的诊断和治疗[J]. 中华眼视光学与视觉科学杂志, 2018, 20(1): 7-13.
Yun'e Zhao, Man Hu. Attaching Importance to Diagnosis and Treatment of Persistent Fetal Vasculature. Chinese Journal of Optometry Ophthalmology and Visual science, 2018, 20(1): 7-13. DOI: 10.3760/cma.j.issn.1674-845X.2018.01.002
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